foodsystFood systemsПищевые системы2618-97712618-7272Федеральный научный центр пищевых систем им. В.М. Горбатова РАН10.21323/2618-9771-2020-3-4-20-23foodsyst-89Research ArticleСтатьиMethodological aspects of the use of dry components of chicken eggs for feeding children with phenylketonuriahttps://orcid.org/0000-0002-6483-1319BykovaS. T.

Svetlana T. Bykova — candidate of technical sciences, Scientific Secretary

140051, Moscow region, Kraskovo, Nekrasov str., 11.

vniik@arrisp.ruhttps://orcid.org/0000-0002-9751-6315KalininaT. G.

Tamara G. Kalinina — candidate of technical sciences, leading researcher, Department of biodegradable polymers, technological tests and experimental production

140051, Moscow region, Kraskovo, Nekrasov str., 11.

vniik@arrisp.ruhttps://orcid.org/0000-0001-9893-9291BushuevaT. V.

Tatyana V. Bushueva– doctor of medical sciences, leading researcher, Laboratory of nutrition of a healthy and sick child

119991, Moscow, Lomonosov avenue, 2, Build. 1;115522, Moscow, Moskvorechye str., 1

tbushueva1@yandex.ruhttps://orcid.org/0000-0002-0603-3394BorovikT. E.

Tatyana E. Borovik — doctor of medical sciences, professor, Head of the laboratory of nutrition of a healthy and sick child

119991, Moscow, Lomonosov avenue, 2, Build. 1;119991, Moscow, Trubetskaya str. 8–2

nutrborovik@mail.ruAll-Russian Research Institute for Starch Products — Branch of V. M. Gorbatov Federal Research Center for Food Systems of Russian Academy of SciencesRussian FederationScientific Center of Children’s Health; Research Centre for Medical GeneticsRussian FederationScientific Center of Children’s Health; I.M. Sechenov First Moscow State Medical University (Sechenov University)Russian Federation202013012021342023Copyright © Bykova S.T., Kalinina T.G., Bushueva T.V., Borovik T.E., 20212021Bykova S.T., Kalinina T.G., Bushueva T.V., Borovik T.E.Bykova S.T., Kalinina T.G., Bushueva T.V., Borovik T.E.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.fsjour.com/jour/article/view/89

Currently, one of the most important tasks facing science and production is the creation of functional product technologies for use in different diets of the population in order to preserve and improve health, as well as reduce the risks and consequences of various diseases, including hereditary ones, such as phenylketonuria (PKU). The All-Russian Research Institute of Starch Products develops technologies for the production of low-protein starch-based products/semi-products enriched with functional ingredients and intended for therapeutic nutrition of patients with PKU. As part of the pilot production, the production of these products is organized. Purpose of work:to justify the possibility of using dry components of chicken eggs (melange, protein, yolk) to enrich low-protein starch products (noodles, vermichel, «spider») intended for feeding children over 3 years old with phenylketonuria;evaluate organoleptic properties and efficiency of low-protein starch products enriched in hypophenylalanine diet of patients with phenylketonuria older than 3 years.

phenylketonuriadietary nutritionlow-protein pastadry egg products (melangeproteinyolk)The article was published as part of the research topic No. 0585–2019–0031-C-01 of the state as-assignment of the V. M. Gorbatov Federal Research Center for Food Systems of RAS and Research «Scientific justification and development of modern methods of dietary therapy for various diseases in children in a multidisciplinary hospital using specialized children’s foods» FSAU «National Medical Research Center for Child Health»ReferencesBykova, S.T., Buravlyova, T.N. (2011). Using the dry ingredients to egg dressing low-protein starch. Storage and processing of farm products, 10, 70–72. (In Russian)Bykova, S.T., Buravlyova, T.N. (2011). Using the dry ingredients to egg dressing low-protein starch. Storage and processing of farm products, 10, 70–72. (In Russian)Bykova, S.T., Buravleva, T.N., Kalinina, T.E., Borovik, T. V. Food composition for the preparation of infant foods. Patent RF, no. 2462050, 2012. 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Dietotherapy of Classical Phenylketonuria: Criteria for Choosing Specialized Phenylalanine-Free Products. Current Pediatrics, 12(5), 40–48. (In Russian)Borovik, T.E., Ladodo, K.S., Bushueva, T.V., Timofeeva, A.G., Kon’, I. Ya., Kruglik, V.I., Volkova, I.N. (2013). Dietotherapy of Classical Phenylketonuria: Criteria for Choosing Specialized Phenylalanine-Free Products. Current Pediatrics, 12(5), 40–48. (In Russian)Phenylketonuria and tetrahydropterin metabolism disorders in children. Clinical recommendations. [Electronic resource: https://www.pediatr-russia.ru/information/klin-rek/deystvuyushchie-klinicheskierekomendatsii/%D0%A4%D0%9A%D0%A3%20_%D0%BA%D0%BB%D0%B8%D0%BD%D1%80%D0%B5%D0%BA%D0%B8_2017.pdf Access date 15.08.2020] (In Russian)Phenylketonuria and tetrahydropterin metabolism disorders in children. Clinical recommendations. [Electronic resource: https://www.pediatr-russia.ru/information/klin-rek/deystvuyushchie-klinicheskierekomendatsii/%D0%A4%D0%9A%D0%A3%20_%D0%BA%D0%BB%D0%B8%D0%BD%D1%80%D0%B5%D0%BA%D0%B8_2017.pdf Access date 15.08.2020] (In Russian)Bushueva, T. V., Borovik, T. E., Fisenko, A. P., Baranov, A. A., Kuzenkova, L. M., Zvonkova, N. G., Timofeeva, A. G., Diakonova, E. Yu., Sattarova, V. V. (2018). Specialized medical nutrition products for children with phenylketonuria. Moscow: Scientific Center of Children’s Health. — 128 p. ISBN978–5–9500392–8–7 (In Russian)Bushueva, T. V., Borovik, T. E., Fisenko, A. P., Baranov, A. A., Kuzenkova, L. M., Zvonkova, N. G., Timofeeva, A. G., Diakonova, E. Yu., Sattarova, V. V. (2018). Specialized medical nutrition products for children with phenylketonuria. Moscow: Scientific Center of Children’s Health. — 128 p. ISBN978–5–9500392–8–7 (In Russian)Borovik, T.E., Ladodo, K.S. (2015). Clinical dietetics of children. A guide for physicians. Moscow: MIA.-720 p. ISBN 978–5–9986–0225–2 (In Russian)Borovik, T.E., Ladodo, K.S. (2015). Clinical dietetics of children. A guide for physicians. Moscow: MIA.-720 p. ISBN 978–5–9986–0225–2 (In Russian)

The authors declare that there are no conflicts of interest present.