foodsystFood systemsПищевые системы2618-97712618-7272Федеральный научный центр пищевых систем им. В.М. Горбатова РАН10.21323/2618-9771-2019-2-3-20-22foodsyst-47Research ArticleСтатьиLOW-PROTEIN PASTA FOR CHILDREN PATIENTS WITH PHENYLKETONURIALOW-PROTEIN PASTA FOR CHILDREN PATIENTS WITH PHENYLKETONURIABykovaS. T.BykovaS. T.

Svetlana T. Bykova — candidate of technical sciences, Scientific Secretary

140051, Moscow region, Kraskovo, Nekrasov str., 11

Svetlana T. Bykova — candidate of technical sciences, Scientific Secretary

140051, Moscow region, Kraskovo, Nekrasov str., 11

vniik@arrisp.ruKalininaT. G.KalininaT. G.

Tamara G. Kalinina — Candidate of Technical Sciences, leading researcher of the department of biodegradable polymers, technological tests and experimental production

140051, Moscow region, Kraskovo, Nekrasov str., 11

Tamara G. Kalinina — Candidate of Technical Sciences, leading researcher of the department of biodegradable polymers, technological tests and experimental production

140051, Moscow region, Kraskovo, Nekrasov str., 11

vniik@arrisp.ruAll-Russian Research Institute for Starch Products — Branch of V. M. Gorbatov Federal Research Center for Food Systems of Russian Academy of SciencesРоссияAll-Russian Research Institute for Starch Products — Branch of V. M. Gorbatov Federal Research Center for Food Systems of Russian Academy of SciencesRussian Federation201905102019232022Copyright © Bykova S.T., Kalinina T.G., 20192019Bykova S.T., Kalinina T.G.Bykova S.T., Kalinina T.G.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.fsjour.com/jour/article/view/47

There are provided data on the work carried out at All-Russian Research Institute for Starch Products to create enriched low-protein pasta based on starch for nutrition the children sick with a phenilketonuria — a hereditary disease (group of fermentopatiya), the bound to violation of amino acids metabolism, mainly phenyl alanine. Optimization of children nutrition is the socially important direction of domestic policy of the Russian Federation since their health directly depends on the good balanced nutrition, especially it is important for the children having diseases of genetic character.

To expand the range of the enriched low-protein food the functional ingredients are picked up, recipes and technology of receiving three types of pasta are developed such as: noodles, vermicelli, «spider line», their nutrition and power values are defined. It is shown that in the received products protein content doesn’t exceed permissible value (<1.0%), fat from 3.3 to 3.6%, ashes — to 0.14%, carbohydrates no more than 88.0% that conforms to requirements imposed to reduced-protein products of baby food.

There are provided data on the work carried out at All-Russian Research Institute for Starch Products to create enriched low-protein pasta based on starch for nutrition the children sick with a phenilketonuria — a hereditary disease (group of fermentopatiya), the bound to violation of amino acids metabolism, mainly phenyl alanine. Optimization of children nutrition is the socially important direction of domestic policy of the Russian Federation since their health directly depends on the good balanced nutrition, especially it is important for the children having diseases of genetic character.

To expand the range of the enriched low-protein food the functional ingredients are picked up, recipes and technology of receiving three types of pasta are developed such as: noodles, vermicelli, «spider line», their nutrition and power values are defined. It is shown that in the received products protein content doesn’t exceed permissible value (<1.0%), fat from 3.3 to 3.6%, ashes — to 0.14%, carbohydrates no more than 88.0% that conforms to requirements imposed to reduced-protein products of baby food.

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The authors declare that there are no conflicts of interest present.